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Количество страниц: 6 с.
Pearson syndrome (PS) is a rare multisystem disease with predominant involvement of the hematopoietic organs, pancreas and liver, developing due to a defect in mitochondrial DNA. Most often, the first clinical manifestations of Pearson syndrome in the form of anemia of varying severity appear in the first year of life. The disease was first described in 1979 by Howard Pearson, who included in this syndrome sideroblastic anemia, vacuolation of hematopoietic progenitor cells in the bone marrow, exocrine pancreatic dysfunction, and early onset of the disease, usually before the age of 1 year. According to the literature, the incidence of Pearson syndrome is 1:5000. This article presents a clinical case of a boy diagnosed with Pearson syndrome at the age of 6 months. The child had pale skin from birth and a general blood test showed severe anemia. In the myelogram: Moderate increase in proliferation of the erythroid germ with impaired maturation, diserythro and dysmegakaryocytopoiesis, moderate monocytosis, ring-shaped sideroblasts 45 %. In a molecular genetic study: on DNA material isolated from the patient’s blood cells and urinary sediment using the polymerase chain reaction of very long fragments, the patient was analyzed for the presence of mitochondrial DNA deletions in the region where most of the major changes were described (m.6380-m. 16567). DNA isolated from the patient’s blood cells and urine sediment revealed a deletion of about 3000 bp. in a homoplasmic state. The boy also has neurological disorders. Currently, the child is admitted monthly to the oncology department of the pediatric center for replacement therapy with blood components. He has been observed by hematologists together with neurologists. He also receives chelation therapy and methylprednisolone therapy on an ongoing basis. For anticonvulsant purposes: vigabatrin. Symptomatic therapy, according to the recommendations of the federal center: Courses of Riboflavin, Tocopherol (vitamin E), Coenzyme Q, Succinic acid, L-carnitine, Thiamine.
Клинический случай синдрома Пирсона у ребенка в Республике Саха (Якутия) / О. В. Ядреева, Е. М. Харабаева, В. Б. Егорова [и др.] ; ГАУ РС (Я) "Республиканская больница N 1 им. М. Е. Николаева", Северо-Восточный федеральный университет им. М. К. Аммосова, Медицинский институт // Вестник Северо-Восточного федерального университета им. М. К. Аммосова. Серия: Медицинские науки. - 2024. - N 2 (35). - C. 70-75. - DOI: 10.25587/2587-5590-2024-2-70-75
DOI: 10.25587/2587-5590-2024-2-70-75
Количество страниц: 8 с.
The article presents the results of a retrospective analysis of hemotransfusion complications according to the acts of official investigations of the commissions of the Ministry of Health that arose during the transfusion of blood components in hospitals of the Republic of Sakha (Yakutia) in the period 1991-2023. The structure, causes and outcomes of hemotransfusion complications are presented. The most common mistakes leading to the development of posttransfusion complications, up to a fatal outcome, were identified. It was found that in the vast majority of the cases, violations during hemotransfusion were observed in district hospitals (70.3 %). Hemotransfusion complications in 12 cases (44.4 %) were associated with of ABO-incompatible transfusion; in 7 (25.9 %) cases - with transfusion of media infected with infection transmitted by hemotransmissive route; in 4 (14.8 %) cases - with transfusion of Rh-factor-incompatible; and in 4 (14.8 %) cases - with transfusion of hemolysed erythrocyte-containing blood components. It was shown that the most common complications of transfusion occurred in surgical (37.1 %) and obstetric departments (29.6 %). In 22.2 % of the cases, complications were detected in therapeutic departments; in 11.1 % - in departments of anesthesiology, intensive care and intensive care. Complications developed more often with transfusion of erythrocyte suspension and were observed in 21 (77.7 %) patients. The occurrence of posttransfusion complications was timely detected in 17 (85 %) patients who received emergency medical care, which led to a successful outcome. In 3 cases, a fatal outcome was recorded, which accounted for 11.1 % of the total number of complications. The causes of hemotransfusion complications are more often non-compliance with the rules for determining the blood group and Rh-factor, as well as non-compliance with the rules for conducting blood compatibility tests of the donor and recipient provided for in the instructions on hemotransfusion; therefore, it was concluded that it is necessary to increase the knowledge and training of medical personnel on transfusion therapy.
Гемотрансфузионные осложнения в медицинских организациях Республики Саха (Якутия) / В. В. Ефремова, Л. А. Апросимов, Л. Е. Давыдова [и др.] ; Северо-Восточный федеральный университет им. М. К. Аммосова, Медицинский институт // Вестник Северо-Восточного федерального университета им. М. К. Аммосова. Серия: Медицинские науки. - 2024. - N 2 (35). - C. 45-52. - DOI: 10.25587/2587-5590-2024-2-45-52
DOI: 10.25587/2587-5590-2024-2-45-52
Количество страниц: 6 с.
- Математика. Естественные науки > Общая биология. Антропология. Вирусология. Микробиология,
- Прикладные науки. Медицина. Ветеринария. Техника. Сельское хозяйство > Медицина > Патология. Клиническая медицина > Инфекционные заболевания,
- НАУКА ЯКУТИИ > МАТЕМАТИКА. ЕСТЕСТВЕННЫЕ НАУКИ > Общая биология. Антропология. Вирусология. Микробиология,
- НАУКА ЯКУТИИ > ПРИКЛАДНЫЕ НАУКИ. МЕДИЦИНА. ТЕХНИКА. СЕЛЬСКОЕ ХОЗЯЙСТВО > Медицина > Патология. Клиническая медицина > Инфекционные заболевания.
This article presents the results of studying the course of tuberculosis infection in children and adolescents who have suffered COVID-19 according to a study of ELISA with the presence of Ig G in the blood. The follow-up included 54 patients aged 2 to 16 years with local forms of tuberculosis who were treated in the inpatient conditions of the children’s department of the E.N. Andreev Scientific and Practical Center of Phthisiology from 2020 to 2022. The patients were divided into two groups: the first group – children who had suffered from COVID-19 according to the results of IgG in the blood – 17 patients; the second group – those who had not had COVID-19 with negative results in IgG blood – 37 patients. A comparative medical and social analysis revealed that children who had had COVID-19 had both social and medical risk factors, as well as a burdened epidemiological history, contact with adult patients with acute progressive and destructive forms of pulmonary tuberculosis. Methods of detecting the tuberculosis process in the first group, 88 % of children were detected by contact, 6 % by treatment, 6 % by immunodiagnostics; in the second group, 51 % by contact, 8 % by treatment and 41 % by immunodiagnostics of the patients. In the study of the tuberculosis process in children of the first group, the infiltration phase was recorded in 80 % patients in the reverse development phase: resorption– 10 % and in the calcification phase – 10 %. In the second group, the infiltration phase was in 50 % of children, the resorption phase was in 14 %, and the calcification phase was in 36 % of patients. It should be noted that the effect of a previously transmitted new coronavirus infection on the course and outcomes of the tuberculosis process was not revealed, no correction of chemotherapy was required, and there was no need to increase the duration of treatment.
Гуляева, Н. А. Течение туберкулеза у детей и подростков, перенесших COVID-19 в условиях Якутии / Н. А. Гуляева, К. Р. Мигалкина, С. С. Саввина ; Северо-Восточный федеральный университет им. М. К. Аммосова, Медицинский институт // Вестник Северо-Восточного федерального университета им. М. К. Аммосова. Серия: Медицинские науки. - 2024. - N 2 (35). - C. 30-35. - DOI: 10.25587/2587-5590-2024-2-30-35
DOI: 10.25587/2587-5590-2024-2-30-35
Количество страниц: 8 с.
- Математика. Естественные науки > Астрономия. Астрофизика. Исследование космического пространства. Геодезия,
- Прикладные науки. Медицина. Ветеринария. Техника. Сельское хозяйство > Управление предприятиями. Организация производства, торговли и транспорта,
- НАУКА ЯКУТИИ > ПРИКЛАДНЫЕ НАУКИ. МЕДИЦИНА. ТЕХНИКА. СЕЛЬСКОЕ ХОЗЯЙСТВО > Управление предприятиями. Организация производства, торговли и транспорта,
- НАУКА ЯКУТИИ > МАТЕМАТИКА. ЕСТЕСТВЕННЫЕ НАУКИ > Астрономия. Астрофизика. Исследование космического пространства. Геодезия.
A spatial analysis of intra-regional transport accessibility of settlements in the Arctic districts of the Sakha Republic (Yakutia) by GIS is an urgent task and can become a necessary support for the processes of decision-making and planning of sustainable development of these territories. The purpose of the study is to perform a spatial analysis of intra- regional transport accessibility of settlements in remote Arctic regions of Yakutia on the example of Anabarsky and Nizhnekolymsky districts. On the basis of the GIS network analysis and calculated coe cients of density of the transport network, the assessment of transport accessibility of the study areas according to winter and summer scenarios was carried out. The automobile and river networks were built on the basis of data from open cartographic sources: OpenStreetMaps and Google Earth Engine, the atlas of highways of the Sakha Republic (Yakutia). On the basis of satellite images of Landsat 5, 8 and Sentinel 2, non- o cial (informal) roads that play an important role in communications between settlements were decrypted and digitized. QGIS and ArcGIS programs were used to perform network analysis and build a map of time availability of the settlements using isochronous method. The created maps clearly show the availability of settlements by time interval. The conducted research made it possible to determine that remote sensing and geoinformation systems are key tools for a spatial analysis of transport infrastructure. Using this tools, it is possible to conduct network analysis of various levels of complexity, as well as build graphs of the transport network, greatly simplifying the counting procedure. The paper tested a method that allows to identify uno cial roads in the Arctic, and the presented methods of GIS analysis and modeling that can be used for further deeper network analytics and graph theory to improve the methodology for studying the transport accessibility of the Republic of Sakha (Yakutia).
Обутов, К. А. Пространственный анализ внутрирайонной транспортной доступности с использованием сетевого ГИС-анализа (на примере Анабарского и Нижнеколымского улусов) / К. А. Обутов, А. Н. Саввинова ; Северо-Восточный федеральный университет им. М. К. Аммосова // Вестник Северо-Восточного федерального университета им. М. К. Аммосова. Серия: Науки о земле. - 2023. - N 4 (32). - C. 111-118. - DOI: 10.25587/2587-8751-2023-4-111-118
DOI: 10.25587/2587-8751-2023-4-111-118
Количество страниц: 9 с.
The article describes a case of the development of a severe form of bronchopulmonary dysplasia in a premature newborn. Globally, about 15 million children are born prematurely every year. On average, it is every tenth child. In Russia, more than 110 thousand children are born prematurely every year, which is about 5.7 % of all newborns per year. [8] This confirms the relevance of the chosen topic. The ABS test falls under the category of express studies, since its parameters change rapidly with any shifts in the patient’s condition (respiratory indicators, body temperature, physical activity, kidney function, etc.). [9] The study of blood pH revealed subcompensated metabolic acidosis, confirming the literature data. The gas composition of the blood varied from hypocapnia to hypercapnia, which indicated a severe degree of respiratory failure with a picture of hypoventilation of the lungs in premature newborns. The revealed decrease in electrolytes was associated with diuretic and steroid therapy used for the patients with bronchopulmonary dysplasia. Due to prematurity, compensatory mechanisms were insufficient to maintain homeostatic parameters (pH, gas and electrolyte composition of blood). When conducting oxygen therapy with a ventilator, it is necessary to be guided by the dynamics of ABS tests to calibrate the parameters of the device and adjust infusion therapy.
Динамика изменения параметров кислотно-основного состояния как основной метод контроля лечения при бронхолегочной дисплазии (на примере клинического случая) / Алексеева С. Н., Макарова А. В., Капитонова А. И. [и др.] ; Северо-Восточный федеральный университет им. М. К. Аммосова, Медицинский институт // Вестник Северо-Восточного федерального университета им. М. К. Аммосова. Серия "Медицинские науки". - 2024. - N 1 (34). - C. 5-13. - DOI: 10.25587/2587-5590-2024-1-5-13
DOI: 10.25587/2587-5590-2024-1-5-13
Количество страниц: 7 с.
Nowadays, dental anomalies in children and teenagers are common pathologies that have a negative impact on the functional state of the organs and tissues of the oral cavity, as well as in general physical development. At the same time, they have a wide range of etiological factors and pathogenetic mechanisms of their development. According to the literature, the problems of occlusion disorders in congenital collagenopathies have not been sufficiently studied, which gave a reason to choose the direction of this research work. Aim. To study the parameters of anatomical deformities of the alveolar process of the upper jaw in deep bite in children and teenagers with various degrees of severity of connective tissue dysplasia. Materials and methods. A study of 306 children and teenagers with DST aged 12-18 years was conducted, of which 157 boys and 149 girls. Deep bite was diagnosed in 124 schoolchildren. The degree of DST was determined by the method of T. Milkovska-Dmitrova and A. Karkashev (1985). At the medical appointment, after determining the dental status, there was performed a biometric study on plaster models of the patient. To obtain objective data, there was used the standard Pon and Tone method. Results. Of all the examined groups of children and adolescents with DST, 37.92+1.08 % with deep bite were diagnosed, where the indicator of mild DST was at the level of 41.94+1.01 %, and moderate and severe 30.64+1.21 % and 27.42+1.26 %, respectively. The dynamics of the average statistical data of the premolar index shows an increasing trend for the severity of anatomical deformities of the alveolar process of the upper jaw in the form of narrowing. The dynamics of the molar index at various degrees of severity of DST determines that with a mild degree, narrowing was observed, whereas with an average degree, pronounced expansion of the alveolar process of the upper jaw was diagnosed, where this value decreases to a severe degree. Conclusions. The established parameters of the values of anatomical deformities of the alveolar process of the upper jaw in deep bite, depending on the severity of DST in children and adolescents, contribute to timely diagnosis and prompt implementation of therapeutic and preventive measures, which accordingly eliminates or minimizes long-term complications of local phenotypic manifestations of congenital collagenopathy.
Клиническая И. Д. характеристика глубокого прикуса у подростков при различных степенях тяжести дисплазии соединительной ткани / Ушницкий И. Д., Давыдова М. М., Никифорова Е. Ю. [и др.] ; Северо-Восточный федеральный университет им. М. К. Аммосова, Медицинский институт // Вестник Северо-Восточного федерального университета им. М. К. Аммосова. Серия: Медицинские науки - 2024. - N 1 (34). - C. 42-48. - DOI: 10.25587/2587-5590-2024-1-42-48
DOI: 10.25587/2587-5590-2024-1-42-48
Количество страниц: 7 с.
Хафизова, А. М. Когнитивные нарушения при наследственных атаксиях (обзор литературы) / Хафизова А. М., Давыдова Т. К., Варламова М. А. ; Якутский научный центр комплексных медицинских проблем // Вестник Северо-Восточного федерального университета им. М. К. Аммосова. Серия "Медицинские науки". - 2024. - N 1 (34). - C. 49-55. - DOI: 10.25587/2587-5590-2024-1-49-55
DOI: 10.25587/2587-5590-2024-1-49-55
Количество страниц: 8 с.
Smoking and vaping are common bad habits, especially among young people. Studying this phenomenon among students is important for developing programs to prevent smoking initiation and help in quitting it. These programs can help improve youth health and reduce the risk of serious illnesses. Purpose: to study the prevalence of smoking traditional cigarettes and electronic cigarettes (including vaping) among 1st-year students of the Ammosov North-Eastern Federal University. The study covered 152 1st-year students of one of the educational departments of the North-Eastern Federal University aged 17 to 30 years (average age 20.62±2.97). A data analysis was performed using the IBM SPSS Statistics software package. A comparison of two groups according to a quantitative indicator with a normal distribution, provided that variances were equal, was performed using Student’s t-test. The share of non-smoking respondents slightly prevailed - 61.8 % (94). The proportion of smokers was 39.2 % (58), of which 35 women (60.34 %), 23 men (39.65 %), the average age of women and men was 20.6 ± 3.03 and 20.65 years, respectively. The smoking experience in men was significantly higher: the average smoking experience in men was 6.48±5.18 years, in women -3.17±2.53 (p=0.002). Thus, men started smoking on average at 14.17±3.96 years, women - at 17.43±3.62 (p=0.002). The smoking index ranged from values close to zero to 7.2 pack/years (mean value - 1.23±1.62 pack/years). The results showed that the majority of respondents noted an increased desire to smoke in a state of stress - 40 (69 %), shortness of breath - 30 (51.7 %), skin problems - 26 (44.8 %), fatigue - 25 (43.1 %), gastrointestinal disorders - 16 (27.6 %), “lump” in the throat - 15 (25.9 %), cough - 22 (37.9 %), frequent headaches 20 (34.5 %), blurred vision - 14 (24.1 %), and attacks of suffocation - 5 (8.6 %). None of the symptoms were noticed in 6 out of 58 (10 %) respondents. The majority of students who combine smoking with vaping do not plan to give up the bad habit (73.07 %), students smoking traditional cigarettes also showed a high percentage of adherence to the bad habit, with 50 % not planning to give up smoking. Thus, this study highlights the need to develop programs to prevent smoking initiation and help to quit among students, which can help improve the health of young people and reduce the risk of serious diseases.
Распространенность курения среди студентов СВФУ / Соловьева Ю. А., Трифонова Е. Н., Романова А. А. [и др.] ; Северо-Восточный федеральный университет им. М. К. Аммосова, Медицинский институт // Вестник Северо-Восточного федерального университета им. М. К. Аммосова. - 2024. - N 1 (34). - C. 62-69. - DOI: 10.25587/2587-5590-2024-1-62-69
DOI: 10.25587/2587-5590-2024-1-62-69
Количество страниц: 3 с.
Regular practice of breathing exercises helps to improve the quality of breathing, increase pulmonary ventilation, improve tissue oxygenation and accelerate the removal of carbon dioxide. This contributes to a more efficient supply of oxygen to organs and tissues, which is especially important during physical training. Hypoxic training, which is carried out in conditions of reduced oxygen content, also has a positive effect on the body. As a result, the body's endurance increases, the aerobic power index and overall physical fitness improve. Thus, the use of various methods of influencing the body through the respiratory system allows you to increase the effectiveness of training loads and achieve higher sports results. The purpose of this article is to evaluate the effect of breathing exercises on the level of lactic acid in the body. The objectives are to identify the effectiveness of breathing exercises aimed at restoring the body after physical activity by measuring the level of lactic acid in capillary blood. Methods of analysis of breathing exercises, medical and biological methods were used. The result of the study showed that the level of lactate is associated with the effect of breathing exercises on blood circulation and oxygen saturation of body cells.
Колодезникова, С. И. Оценка влияния дыхательной гимнастики на уровень молочной кислоты у спортсменов / Колодезникова С. И. ; Северо-Восточный федеральный университет им. М. К. Аммосова // Глобальный научный потенциал. - 2023. - N 9 (150). - С. 61-63.
Количество страниц: 5 с.
- Общественные науки. Образование > Народное образование. Воспитание. Обучение. Организация досуга > Высшее образование. Высшая школа. Подготовка научных кадров,
- Прикладные науки. Медицина. Ветеринария. Техника. Сельское хозяйство > Медицина,
- НАУКА ЯКУТИИ > ОБЩЕСТВЕННЫЕ НАУКИ > Народное образование. Воспитание. Обучение. Организация досуга > Высшее образование. Высшая школа. Подготовка научных кадров,
- НАУКА ЯКУТИИ > ПРИКЛАДНЫЕ НАУКИ. МЕДИЦИНА. ТЕХНИКА. СЕЛЬСКОЕ ХОЗЯЙСТВО > Медицина.
The article aims to study the influence of the Olympiad activities on the quality of acquiring general professional competencies in students of the department "Pediatrics" of the Medical Institute of North-Eastern Federal University. The objectives are to compose tasks, analyze the results of the Olympiad, and make recommendations on how to improve the conduct of the Olympiad. To achieve the objectives, an analysis of the compiled tasks and the results of the Olympiad for three years was carried out. The authors used the method of comparative analysis. The hypothesis was confirmed that the Olympiad activity significantly increases the motivation for acquiring general professional competencies, which will be the basis for the future professional activity of a doctor. In the conditions of higher professional education, the integration relationship between the humanities and natural disciplines is of particular attention; this is the relevance of this study. The analysis of the results of the Olympiad and the results of academic performance in the disciplines "Latin with the basics of medical terminology" and "Pathophysiology" showed that every year the Olympiad is gaining popularity: the number of participants is growing, the methods of organizing and conducting are being improved, and the tasks of the Olympiad are being revised. The organizers of the Olympiad noted the improvement in the results of the Olympiad. Despite the decrease in the number of winners of the Olympiad, there is an increase in the average score from 37.8 to 43 (out of the maximum 50 points). This is due to the increase in the average score of the participants in the second round from 20 to 26 points. Every year the increase in the number of participants leads to increased competition for prizes. Taking into account the results of the study, measures were recommended to improve the quality of the Olympiad.
Алексеева, С. Н. Влияние олимпиадной деятельности на качество приобретения общепрофессиональных компетенций у студентов отделения "Педиатрия" / Алексеева С. Н., Антипина У. Д., Дмитриева О.Н. ; Северо-Восточный федеральный университет им. М. К. Аммосова // Глобальный научный потенциал. - 2022. - N 12 (141). - С. 59-63.